Gerstmann's syndrome

Medline NLM definition for Gerstmann Straussler Scheinker syndrome:  Familially occurring neurodegenerative condition that has morphological similarities to CREUTZFELDT-JAKOB SYNDROME. In Gerstmann-Straussler syndrome there is slower progression, signs of spinocerebellar ataxia, and the spongiosis is less pronounced. Prion proteins and amyloid plaques are found in the brain of patients with the syndrome. A germline mutation of the prion protein has been demonstrated.

Gerstmann's syndrome: factsheet from NINDS, the National Institute of Neurological Disorders and Stroke (US site)

Gerstmann Syndrome: information from NORD, the National Organization for Rare Disorders (US site)

Creutzfeldt-Jakob Disease (CJD): factsheet from NINDS, the National Institute of Neurological Disorders and Stroke (US site)

Creutzfeldt-Jakob Disease (CJD): information from the NHS website

Creutzfeldt-Jakob Disease (CJD): information from Patient UK website

PubMed (Medline) search on Gerstmann's syndrome

Support Groups

See Creutzfeldt-Jakob Disease patient page.

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